"Fructose Intolerance" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
An autosomal recessive fructose metabolism disorder due to deficient fructose-1-phosphate aldolase (EC 2.1.2.13) activity, resulting in accumulation of fructose-1-phosphate. The accumulated fructose-1-phosphate inhibits glycogenolysis and gluconeogenesis, causing severe hypoglycemia following ingestion of fructose. Prolonged fructose ingestion in infants leads ultimately to hepatic failure and death. Patients develop a strong distaste for sweet food, and avoid a chronic course of the disease by remaining on a fructose- and sucrose-free diet.
| Descriptor ID |
D005633
|
| MeSH Number(s) |
C16.320.565.202.251.271 C18.452.648.202.251.271
|
| Concept/Terms |
Fructose Intolerance- Fructose Intolerance
- Fructose Intolerances
- Intolerance, Fructose
- Intolerances, Fructose
- Fructose Aldolase B Deficiency
- Fructose Intolerance, Hereditary
- Fructose Intolerances, Hereditary
- Hereditary Fructose Intolerances
- ALDOB Deficiency
- ALDOB Deficiencies
- Deficiencies, ALDOB
- Deficiency, ALDOB
- Fructose-1,6-Bisphosphate Aldolase B Deficiency
- Fructose 1,6 Bisphosphate Aldolase B Deficiency
- Fructose-1-Phosphate Aldolase Deficiency
- Aldolase Deficiencies, Fructose-1-Phosphate
- Aldolase Deficiency, Fructose-1-Phosphate
- Deficiencies, Fructose-1-Phosphate Aldolase
- Deficiency, Fructose-1-Phosphate Aldolase
- Fructose 1 Phosphate Aldolase Deficiency
- Fructose-1-Phosphate Aldolase Deficiencies
- Fructosemia
- Fructosemias
- Hereditary Fructose Intolerance
- Aldolase B Deficiency
- Aldolase B Deficiencies
- Deficiencies, Aldolase B
- Deficiency, Aldolase B
- Fructose-1,6-Biphosphate Aldolase Deficiency
- Aldolase Deficiencies, Fructose-1,6-Biphosphate
- Aldolase Deficiency, Fructose-1,6-Biphosphate
- Deficiencies, Fructose-1,6-Biphosphate Aldolase
- Deficiency, Fructose-1,6-Biphosphate Aldolase
- Fructose 1,6 Biphosphate Aldolase Deficiency
- Fructose-1,6-Biphosphate Aldolase Deficiencies
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Below are MeSH descriptors whose meaning is more general than "Fructose Intolerance".
Below are MeSH descriptors whose meaning is more specific than "Fructose Intolerance".
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